Abnormalities seen in the four-chamber view

In this condition, the position of the tricuspid valve is normal but the leaflets are dysplastic. The tricuspid valve is incompetent, demonstrated by colour Doppler showing tricuspid regurgitation, and the right atrium is dilated. Significant cardiomegaly may cause secondary lung compression and consequent hypoplasia. Severe cases can result in fetal hydrops and subsequent death. In severe cases of tricuspid valve dysplasia there is pulmonary stenosis or functional atresia.

Prevalence

This defect is found in less than 1 in 20,000 live births.

Other abnormalities

This defect is commonly associated with chromosomal anomalies, mainly Trisomy 18.

Prognosis

If cardiac anomaly is isolated, prognosis is guarded in those cases where there is a severe tricuspid valve regurgitation and cardiomegaly.